A peripapillary staphyloma case presenting with unilateral non-fixing eye

Peripapillary staphyloma (PPS) is a non-hereditary congenital optic disc (OD) anomaly. Herein, we aimed to describe a case of PPS and discuss the clinical, orbital magnetic resonance imaging (MRI) and ultra sonography (USG) findings. A one-year-old healthy girl was referred to our hospital for absence of fixation in her left eye. In addition to ophthalmological examinations, MRI and ocular USG were also performed. Sciascopic examination revealed -2.0 diopters in her right and -8.0 diopters in her left eye. Slit-lamp examination showed normal findings in both eyes. At fundus examination, peripapillary staphyloma was detected in the left eye, while the right eye showed normal findings. MRI and USG also supported the diagnosis. As a result, MRI and USG findings can support the clinical observations in the diagnosis of PPS, which should be kept in mind especially in the differential diagnosis of unilateral absence of fixation in children.